Chapter XIV
Diseases of the genitourinary system
(N00-N99)

Rules Conventions GCS

Glomerular diseases
(N00-N08)

Coding-Hint
Use additional code, if desired, to identify associated chronic kidney disease ( N18.-) .
Use additional code, if desired, to identify external cause (Chapter XX) or presence of renal failure, Acute ( N17.-), or Unspecified ( N19) .
Excl.:
hypertensive renal disease ( I12.-)
Modifiers

The following fourth-character subdivisions classify morphological changes and are for use with categories N00-N07. Subdivisions .0-.8 should not normally be used unless these have been specifically identified (e.g. by renal biopsy or autopsy). The three-character categories relate to clinical syndromes.

Code Title
.0
Minor glomerular abnormality
Incl.:
Minimal change lesion
.1
Focal and segmental glomerular lesions
Incl.:
Focal and segmental:
  • hyalinosis
  • sclerosis
Focal glomerulonephritis
.2
Diffuse membranous glomerulonephritis
.3
Diffuse mesangial proliferative glomerulonephritis
.4
Diffuse endocapillary proliferative glomerulonephritis
.5
Diffuse mesangiocapillary glomerulonephritis
Incl.:
Membranoproliferative glomerulonephritis, types 1 and 3, or NOS
.6
Dense deposit disease
Incl.:
Membranoproliferative glomerulonephritis, type 2
.7
Diffuse crescentic glomerulonephritis
Incl.:
Extracapillary glomerulonephritis
.8
Other
Incl.:
Proliferative glomerulonephritis NOS
.9
Unspecified

N00 Acute nephritic syndrome
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
acute:
  • glomerular disease
  • glomerulonephritis
  • nephritis
  • renal disease NOS
Excl.:
acute infectious tubulo-interstitial nephritis ( N10)
nephritic syndrome NOS ( N05.-)

N01 Rapidly progressive nephritic syndrome
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
rapidly progressive:
  • glomerular disease
  • glomerulonephritis
  • nephritis
Excl.:
nephritic syndrome NOS ( N05.-)

N02 Recurrent and persistent haematuria
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
haematuria:
  • benign (familial)(of childhood)
  • with morphological lesion specified in .0-.8 before N00.-
Excl.:
haematuria NOS ( R31)

N03 Chronic nephritic syndrome
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
chronic:
  • glomerular disease
  • glomerulonephritis
  • nephritis
Excl.:
chronic tubulo-interstitial nephritis ( N11.-)
diffuse sclerosing glomerulonephritis ( N18.-)
nephritic syndrome NOS ( N05.-)

N04 Nephrotic syndrome
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
congenital nephrotic syndrome
lipoid nephrosis

N05 Unspecified nephritic syndrome
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
  • glomerular disease
  • glomerulonephritis
  • nephritis
  • NOS
nephropathy NOS and renal disease NOS with morphological lesion specified in .0-.8 before N00.-
Excl.:
nephropathy NOS with no stated morphological lesion ( N28.9)
renal disease NOS with no stated morphological lesion ( N28.9)
tubulo-interstitial nephritis NOS ( N12)

N06 Isolated proteinuria with specified morphological lesion
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Incl.:
proteinuria (isolated)(orthostatic)(persistent) with morphological lesion specified in .0-.8 before N00.-
Excl.:
proteinuria:

N07 Hereditary nephropathy, not elsewhere classified
DCS.IX.2

Modifier-Hint
[See before N00 for subdivisions]
Excl.:
Alport syndrome ( Q87.8)
hereditary amyloid nephropathy ( E85.0)
nail patella syndrome ( Q87.2)
non-neuropathic heredofamilial amyloidosis ( E85.0)

N08* Glomerular disorders in diseases classified elsewhere

Incl.:
nephropathy in diseases classified elsewhere
Excl.:
renal tubulo-interstitial disorders in diseases classified elsewhere ( N16.-*)
N08.0* Glomerular disorders in infectious and parasitic diseases classified elsewhere
Incl.:
Glomerular disorders in:
N08.1* Glomerular disorders in neoplastic diseases
Incl.:
Glomerular disorders in:
N08.2* Glomerular disorders in blood diseases and disorders involving the immune mechanism
Incl.:
Glomerular disorders in:
  • cryoglobulinaemia (D89.1†)
  • disseminated intravascular coagulation [defibrination syndrome] (D65†)
  • haemolytic-uraemic syndrome (D59.3†)
  • Henoch(-Schönlein) purpura (D69.0†)
  • sickle-cell disorders (D57.-†)
N08.3* Glomerular disorders in diabetes mellitus (E10-E14 with common fourth character .2†)
N08.4* Glomerular disorders in other endocrine, nutritional and metabolic diseases
Incl.:
Glomerular disorders in:
N08.5* Glomerular disorders in systemic connective tissue disorders
Incl.:
Glomerular disorders in:
N08.8* Glomerular disorders in other diseases classified elsewhere
Incl.:
Glomerular disorders in subacute bacterial endocarditis ( I33.0†)