Chapter IX
Diseases of the circulatory system
(I00-I99)

Rules Conventions GCS

Other forms of heart disease
(I30-I52)

I30 Acute pericarditis
DCS.IX.10

Incl.:
acute pericardial effusion
Excl.:
rheumatic pericarditis (acute) ( I01.0)
I30.0 Acute nonspecific idiopathic pericarditis
I30.1 Infective pericarditis
Incl.:
Pericarditis:
  • pneumococcal
  • purulent
  • staphylococcal
  • streptococcal
  • viral
Pyopericarditis
Coding-Hint
Use additional code (B95-B98), if desired, to identify infectious agent.
I30.8 Other forms of acute pericarditis
I30.9 Acute pericarditis, unspecified

I31 Other diseases of pericardium
DCS.IX.10

Excl.:
current complications following acute myocardial infarction ( I23.-)
postcardiotomy syndrome ( I97.0)
trauma ( S26.-)
when specified as rheumatic ( I09.2)
I31.0 Chronic adhesive pericarditis
Incl.:
Accretio cordis
Adherent pericardium
Adhesive mediastinopericarditis
I31.1 Chronic constrictive pericarditis
Incl.:
Concretio cordis
Pericardial calcification
I31.2 Haemopericardium, not elsewhere classified
I31.3 Pericardial effusion (noninflammatory)
Incl.:
Chylopericardium
I31.8 Other specified diseases of pericardium
Incl.:
Epicardial plaques
Focal pericardial adhesions
I31.9 Disease of pericardium, unspecified
Incl.:
Cardiac tamponade
Pericarditis (chronic) NOS

I32* Pericarditis in diseases classified elsewhere
DCS.IX.10

I32.0* Pericarditis in bacterial diseases classified elsewhere
Incl.:
Pericarditis:
I32.1* Pericarditis in other infectious and parasitic diseases classified elsewhere
I32.8* Pericarditis in other diseases classified elsewhere
Incl.:
Pericarditis (in):

I33 Acute and subacute endocarditis
DCS.IX.10

Excl.:
acute rheumatic endocarditis ( I01.1)
endocarditis NOS ( I38)
I33.0 Acute and subacute infective endocarditis
Incl.:
Endocarditis (acute)(subacute):
  • bacterial
  • infective NOS
  • lenta
  • malignant
  • septic
  • ulcerative
Coding-Hint
Use additional code (B95-B98), if desired, to identify infectious agent.
I33.9 Acute endocarditis, unspecified
Incl.:
  • Endocarditis
  • Myoendocarditis
  • Periendocarditis
  • acute or subacute

I34 Nonrheumatic mitral valve disorders
DCS.IX.10

Excl.:
mitral (valve):
when of unspecified cause but with mention of:
  • diseases of aortic valve (I08.0)
  • mitral stenosis or obstruction (I05.0)
when specified as congenital ( Q23.2-Q23.9)
when specified as rheumatic ( I05.-)
I34.0 Mitral (valve) insufficiency
Incl.:
  • Mitral (valve):
    • incompetence
    • regurgitation
  • NOS or of specified cause, except rheumatic
I34.1 Mitral (valve) prolapse
Incl.:
Floppy mitral valve syndrome
Excl.:
Marfan syndrome ( Q87.4)
I34.2 Nonrheumatic mitral (valve) stenosis
I34.8 Other nonrheumatic mitral valve disorders
I34.9 Nonrheumatic mitral valve disorder, unspecified

I35 Nonrheumatic aortic valve disorders
DCS.IX.10

Excl.:
hypertrophic subaortic stenosis ( I42.1)
when of unspecified cause but with mention of diseases of mitral valve ( I08.0)
when specified as congenital ( Q23.0, Q23.1, Q23.4-Q23.9)
when specified as rheumatic ( I06.-)
I35.0 Aortic (valve) stenosis
I35.1 Aortic (valve) insufficiency
Incl.:
  • Aortic (valve):
    • incompetence
    • regurgitation
  • NOS or of specified cause, except rheumatic
I35.2 Aortic (valve) stenosis with insufficiency
I35.8 Other aortic valve disorders
I35.9 Aortic valve disorder, unspecified

I36 Nonrheumatic tricuspid valve disorders
DCS.IX.10

Excl.:
when of unspecified cause ( I07.-)
when specified as congenital ( Q22.4, Q22.8, Q22.9)
when specified as rheumatic ( I07.-)
I36.0 Nonrheumatic tricuspid (valve) stenosis
I36.1 Nonrheumatic tricuspid (valve) insufficiency
Incl.:
  • Tricuspid (valve):
    • incompetence
    • regurgitation
  • of specified cause, except rheumatic
I36.2 Nonrheumatic tricuspid (valve) stenosis with insufficiency
I36.8 Other nonrheumatic tricuspid valve disorders
I36.9 Nonrheumatic tricuspid valve disorder, unspecified

I37 Pulmonary valve disorders
DCS.IX.10

Excl.:
when specified as congenital ( Q22.1, Q22.2, Q22.3)
when specified as rheumatic ( I09.8)
I37.0 Pulmonary valve stenosis
I37.1 Pulmonary valve insufficiency
Incl.:
  • Pulmonary valve:
    • incompetence
    • regurgitation
  • NOS or of specified cause, except rheumatic
I37.2 Pulmonary valve stenosis with insufficiency
I37.8 Other pulmonary valve disorders
I37.9 Pulmonary valve disorder, unspecified

I38 Endocarditis, valve unspecified
DCS.IX.10

Incl.:
Endocarditis (chronic) NOS
  • Valvular:
    • incompetence
    • insufficiency
    • regurgitation
    • stenosis
  • Valvulitis (chronic)
  • of unspecified valve
  • NOS or of specified cause, except rheumatic or congenital
Excl.:
congenital insufficiency of cardiac valve NOS ( Q24.8)
congenital stenosis of cardiac valve NOS ( Q24.8)
endocardial fibroelastosis ( I42.4)
when specified as rheumatic ( I09.1)

I39* Endocarditis and heart valve disorders in diseases classified elsewhere
DCS.IX.10

Incl.:
endocardial involvement in:
I39.0* Mitral valve disorders in diseases classified elsewhere
I39.1* Aortic valve disorders in diseases classified elsewhere
I39.2* Tricuspid valve disorders in diseases classified elsewhere
I39.3* Pulmonary valve disorders in diseases classified elsewhere
I39.4* Multiple valve disorders in diseases classified elsewhere
I39.8* Endocarditis, valve unspecified, in diseases classified elsewhere

I40 Acute myocarditis
DCS.IX.10

I40.0 Infective myocarditis
Incl.:
Septic myocarditis
Coding-Hint
Use additional code (B95-B98), if desired, to identify infectious agent.
I40.1 Isolated myocarditis
I40.8 Other acute myocarditis
I40.9 Acute myocarditis, unspecified

I41* Myocarditis in diseases classified elsewhere
DCS.IX.10

I41.0* Myocarditis in bacterial diseases classified elsewhere
Incl.:
Myocarditis:
I41.1* Myocarditis in viral diseases classified elsewhere
Incl.:
Influenzal myocarditis (acute):
  • seasonal virus identified (J10.8†)
  • virus not identified (J11.8†)
  • zoonotic or pandemic influenza virus identified (J09†)
Mumps myocarditis ( B26.8†)
I41.2* Myocarditis in other infectious and parasitic diseases classified elsewhere
Incl.:
Myocarditis in:
I41.8* Myocarditis in other diseases classified elsewhere
Incl.:
Rheumatoid myocarditis ( M05.3†)
Sarcoid myocarditis ( D86.8†)

I42 Cardiomyopathy
DCS.IX.10

Excl.:
cardiomyopathy complicating:
ischaemic cardiomyopathy ( I25.5)
I42.0 Dilated cardiomyopathy
Incl.:
Congestive cardiomyopathy
I42.1 Obstructive hypertrophic cardiomyopathy
Incl.:
Hypertrophic subaortic stenosis
I42.2 Other hypertrophic cardiomyopathy
Incl.:
Nonobstructive hypertrophic cardiomyopathy
I42.3 Endomyocardial (eosinophilic) disease
Incl.:
Endomyocardial (tropical) fibrosis
Löffler endocarditis
I42.4 Endocardial fibroelastosis
Incl.:
Congenital cardiomyopathy
I42.5 Other restrictive cardiomyopathy
Incl.:
Constrictive cardiomyopathy NOS
I42.6 Alcoholic cardiomyopathy
I42.7 Cardiomyopathy due to drugs and other external agents
Coding-Hint
Use additional external cause code (Chapter XX), if desired, to identify cause.
I42.8 Other cardiomyopathies
I42.9 Cardiomyopathy, unspecified
Incl.:
Cardiomyopathy (primary)(secondary) NOS

I43* Cardiomyopathy in diseases classified elsewhere
DCS.IX.10

I43.0* Cardiomyopathy in infectious and parasitic diseases classified elsewhere
Incl.:
Cardiomyopathy in diphtheria ( A36.8†)
I43.1* Cardiomyopathy in metabolic diseases
Incl.:
Cardiac amyloidosis ( E85.-†)
I43.2* Cardiomyopathy in nutritional diseases
Incl.:
Nutritional cardiomyopathy NOS ( E63.9†)
I43.8* Cardiomyopathy in other diseases classified elsewhere
Incl.:
Gouty tophi of heart ( M10.0†)
Thyrotoxic heart disease ( E05.9†)

I44 Atrioventricular and left bundle-branch block
DCS.IX.10

I44.0 Atrioventricular block, first degree
I44.1 Atrioventricular block, second degree
Incl.:
Atrioventricular block, type I and II
Möbitz block, type I and II
Second-degree block, type I and II
Wenckebach block
I44.2 Atrioventricular block, complete
Incl.:
Complete heart block NOS
Third-degree block
I44.3 Other and unspecified atrioventricular block
Incl.:
Atrioventricular block NOS
I44.4 Left anterior fascicular block
I44.5 Left posterior fascicular block
I44.6 Other and unspecified fascicular block
Incl.:
Left bundle-branch hemiblock NOS
I44.7 Left bundle-branch block, unspecified

I45 Other conduction disorders
DCS.IX.10

I45.0 Right fascicular block
I45.1 Other and unspecified right bundle-branch block
Incl.:
Right bundle-branch block NOS
I45.2 Bifascicular block
I45.3 Trifascicular block
I45.4 Nonspecific intraventricular block
Incl.:
Bundle-branch block NOS
I45.5 Other specified heart block
Incl.:
Sinoatrial block
Sinoauricular block
Excl.:
heart block NOS ( I45.9)
I45.6 Pre-excitation syndrome
Incl.:
Anomalous atrioventricular excitation
Atrioventricular conduction:
  • accelerated
  • accessory
  • pre-excitation
Lown-Ganong-Levine syndrome
Wolff-Parkinson-White syndrome
I45.8 Other specified conduction disorders
Incl.:
Atrioventricular [AV] dissociation
Interference dissociation
Excl.:
prolongation of QT interval ( R94.3)
I45.9 Conduction disorder, unspecified
Incl.:
Heart block NOS
Stokes-Adams syndrome

I46 Cardiac arrest
DCS.IX.8 DCS.IX.10

Excl.:
cardiogenic shock ( R57.0)
complicating:
  • abortion or ectopic or molar pregnancy (O00-O07, O08.8)
  • obstetric surgery and procedures (O75.4)
I46.0 Cardiac arrest with successful resuscitation
I46.1 Sudden cardiac death, so described
Excl.:
sudden death:
I46.9 Cardiac arrest, unspecified

I47 Paroxysmal tachycardia
DCS.IX.10

Excl.:
complicating:
  • abortion or ectopic or molar pregnancy (O00-O07, O08.8)
  • obstetric surgery and procedures (O75.4)
tachycardia:
I47.0 Re-entry ventricular arrhythmia
I47.1 Supraventricular tachycardia
Incl.:
Tachycardia (paroxysmal):
  • atrial
  • atrioventricular [AV]:
    • —  NOS
    • —  re-entrant (nodal) [AVNRT] [AVRT]
  • junctional
  • nodal
I47.2 Ventricular tachycardia
I47.9 Paroxysmal tachycardia, unspecified
Incl.:
Bouveret(-Hoffmann) syndrome

I48 Atrial fibrillation and flutter
DCS.IX.10

I48.0 Paroxysmal atrial fibrillation
I48.1 Persistent atrial fibrillation
I48.2 Chronic atrial fibrillation
I48.3 Typical atrial flutter
Incl.:
Type I atrial flutter
I48.4 Atypical atrial flutter
Incl.:
Type II atrial flutter
I48.9 Atrial fibrillation and atrial flutter, unspecified

I49 Other cardiac arrhythmias
DCS.IX.10

Excl.:
bradycardia:
complicating:
  • abortion or ectopic or molar pregnancy (O00-O07, O08.8)
  • obstetric surgery and procedures (O75.4)
neonatal cardiac dysrhythmia ( P29.1)
I49.0 Ventricular fibrillation and flutter
I49.1 Atrial premature depolarization
Incl.:
Atrial premature beats
I49.2 Junctional premature depolarization
I49.3 Ventricular premature depolarization
I49.4 Other and unspecified premature depolarization
Incl.:
Ectopic beats
Extrasystoles
Extrasystolic arrhythmias
Premature:
  • beats NOS
  • contractions
I49.5 Sick sinus syndrome
Incl.:
Tachycardia-bradycardia syndrome
I49.8 Other specified cardiac arrhythmias
Incl.:
Brugada syndrome
Long QT syndrome
Rhythm disorder:
  • coronary sinus
  • ectopic
  • nodal
I49.9 Cardiac arrhythmia, unspecified
Incl.:
Arrhythmia (cardiac) NOS

I50 Heart failure
DCS.IX.10

Excl.:
complicating:
  • abortion or ectopic or molar pregnancy (O00-O07, O08.8)
  • obstetric surgery and procedures (O75.4)
due to hypertension ( I11.0)
  • with renal disease (I13.-)
following cardiac surgery or due to presence of cardiac prosthesis ( I97.1)
neonatal cardiac failure ( P29.0)
I50.0 Congestive heart failure
Incl.:
Congestive heart disease
Right ventricular failure (secondary to left heart failure)
I50.1 Left ventricular failure
Incl.:
Cardiac asthma
Left heart failure
  • Oedema of lung
  • Pulmonary oedema
  • with mention of heart disease NOS or heart failure
I50.9 Heart failure, unspecified
Incl.:
Cardiac, heart or myocardial failure NOS

I51 Complications and ill-defined descriptions of heart disease
DCS.IX.10

Excl.:
any condition in I51.4-I51.9 due to hypertension ( I11.-)
any condition in I51.4-I51.9 due to hypertension
  • with renal disease (I13.-)
complications following acute myocardial infarction ( I23.-)
when specified as rheumatic ( I00-I09)
I51.0 Cardiac septal defect, acquired
Incl.:
Acquired septal defect (old):
  • atrial
  • auricular
  • ventricular
I51.1 Rupture of chordae tendineae, not elsewhere classified
I51.2 Rupture of papillary muscle, not elsewhere classified
I51.3 Intracardiac thrombosis, not elsewhere classified
Incl.:
Thrombosis (old):
  • apical
  • atrial
  • auricular
  • ventricular
I51.4 Myocarditis, unspecified
DCS.IX.2
Incl.:
Myocardial fibrosis
Myocarditis:
  • NOS
  • chronic (interstitial)
I51.5 Myocardial degeneration
DCS.IX.2
Incl.:
Degeneration of heart or myocardium:
  • fatty
  • senile
Myocardial disease
I51.6 Cardiovascular disease, unspecified
DCS.IX.2
Incl.:
Cardiovascular accident NOS
Excl.:
atherosclerotic cardiovascular disease, so described ( I25.0)
I51.7 Cardiomegaly
DCS.IX.2
Incl.:
Cardiac:
  • dilatation
  • hypertrophy
Ventricular dilatation
I51.8 Other ill-defined heart diseases
DCS.IX.2
Incl.:
Carditis (acute)(chronic)
Pancarditis (acute)(chronic)
I51.9 Heart disease, unspecified
DCS.IX.2

I52* Other heart disorders in diseases classified elsewhere
DCS.IX.10

Excl.:
cardiovascular disorders NOS in diseases classified elsewhere ( I98.-*)
I52.0* Other heart disorders in bacterial diseases classified elsewhere
Incl.:
Meningococcal carditis NEC ( A39.5†)
I52.1* Other heart disorders in other infectious and parasitic diseases classified elsewhere
Incl.:
Pulmonary heart disease in schistosomiasis ( B65.-†)
I52.8* Other heart disorders in other diseases classified elsewhere
Incl.:
Rheumatoid carditis ( M05.3†)