Chapter III
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
(D50-D89)

Rules Conventions GCS

Coagulation defects, purpura and other haemorrhagic conditions
(D65-D69)

D65 Disseminated intravascular coagulation [defibrination syndrome]

Incl.:
Afibrinogenaemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation [DIC]
Fibrinolytic haemorrhage, acquired
Purpura:
  • fibrinolytic
  • fulminans
Excl.:
that (complicating):

D66 Hereditary factor VIII deficiency

Incl.:
Deficiency factor VIII (with functional defect)
Haemophilia:
  • NOS
  • A
  • classical
Excl.:
factor VIII deficiency with vascular defect ( D68.0)

D67 Hereditary factor IX deficiency

Incl.:
Christmas disease
Deficiency:
  • factor IX (with functional defect)
  • plasma thromboplastin component [PTC]
Haemophilia B

D68 Other coagulation defects

Excl.:
those complicating:
D68.0 Von Willebrand disease
Incl.:
Angiohaemophilia
Factor VIII deficiency with vascular defect
Vascular haemophilia
Excl.:
capillary fragility (hereditary) ( D69.8)
factor VIII deficiency:
  • NOS (D66)
  • with functional defect (D66)
D68.1 Hereditary factor XI deficiency
Incl.:
Haemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
D68.2 Hereditary deficiency of other clotting factors
Incl.:
Congenital afibrinogenaemia
Deficiency:
  • AC globulin
  • proaccelerin
Deficiency of factor:
  • I [fibrinogen]
  • II [prothrombin]
  • V [labile]
  • VII [stable]
  • X [Stuart-Prower]
  • XII [Hageman]
  • XIII [fibrin-stabilizing]
Dysfibrinogenaemia (congenital)
Hypoproconvertinaemia
Owren disease
D68.3 Haemorrhagic disorder due to circulating anticoagulants
DCS.III.3
Incl.:
Haemorrhage during long-term use of anticoagulants
Hyperheparinaemia
Increase in:
  • antithrombin
  • anti-VIIIa
  • anti-IXa
  • anti-Xa
  • anti-XIa
Coding-Hint
Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant.
Excl.:
long-term use of anticoagulants without haemorrhage ( Z92.1)
D68.4 Acquired coagulation factor deficiency
Incl.:
Deficiency of coagulation factor due to:
  • liver disease
  • vitamin K deficiency
Excl.:
vitamin K deficiency of newborn ( P53)
D68.5 Primary thrombophilia
Incl.:
Activated protein C resistance [factor V Leiden mutation]
Deficiency:
  • antithrombin
  • protein C
  • protein S
Prothrombin gene mutation
D68.6 Other thrombophilia
Incl.:
Anticardiolipin syndrome
Antiphospholipid syndrome
Presence of the lupus anticoagulant
Excl.:
disseminated intravascular coagulation ( D65)
hyperhomocysteinemia ( E72.1)
D68.8 Other specified coagulation defects
D68.9 Coagulation defect, unspecified

D69 Purpura and other haemorrhagic conditions

Excl.:
benign hypergammaglobulinaemic purpura ( D89.0)
cryoglobulinaemic purpura ( D89.1)
essential (haemorrhagic) thrombocythaemia ( D47.3)
purpura fulminans ( D65)
thrombotic thrombocytopenic purpura ( M31.1)
D69.0 Allergic purpura
Incl.:
Purpura:
  • anaphylactoid
  • Henoch(-Schönlein)
  • nonthrombocytopenic:
    • —  haemorrhagic
    • —  idiopathic
  • vascular
Vasculitis, allergic
D69.1 Qualitative platelet defects
Incl.:
Bernard-Soulier [giant platelet] syndrome
Glanzmann disease
Grey platelet syndrome
Thromboasthenia (haemorrhagic)(hereditary)
Thrombocytopathy
Excl.:
von Willebrand disease ( D68.0)
D69.2 Other nonthrombocytopenic purpura
Incl.:
Purpura:
  • NOS
  • senile
  • simplex
D69.3 Idiopathic thrombocytopenic purpura
Incl.:
Evans syndrome
D69.4 Other primary thrombocytopenia
Excl.:
thrombocytopenia with absent radius ( Q87.2)
transient neonatal thrombocytopenia ( P61.0)
Wiskott-Aldrich syndrome ( D82.0)
D69.5 Secondary thrombocytopenia
Coding-Hint
Use additional external cause code (Chapter XX), if desired, to identify cause.
D69.6 Thrombocytopenia, unspecified
D69.8 Other specified haemorrhagic conditions
Incl.:
Capillary fragility (hereditary)
Vascular pseudohaemophilia
D69.9 Haemorrhagic condition, unspecified