Chapter XVII
Congenital malformations, deformations and chromosomal abnormalities
(Q00-Q99)

Congenital malformations of the urinary system
(Q60-Q64)

Q60 Renal agenesis and other reduction defects of kidney

Incl.:
atrophy of kidney:
  • congenital
  • infantile
congenital absence of kidney
Q60.0 Renal agenesis, unilateral
Q60.1 Renal agenesis, bilateral
Q60.2 Renal agenesis, unspecified
Q60.3 Renal hypoplasia, unilateral
Q60.4 Renal hypoplasia, bilateral
Q60.5 Renal hypoplasia, unspecified
Q60.6 Potter syndrome

Q61 Cystic kidney disease

Excl.:
cyst of kidney (acquired) ( N28.1)
Potter syndrome ( Q60.6)
Q61.0 Congenital single renal cyst
Incl.:
Congenital cyst of kidney (single)
Q61.1 Polycystic kidney, autosomal recessive
Incl.:
Polycystic kidney, infantile type
Q61.2 Polycystic kidney, autosomal dominant
Incl.:
Polycystic kidney, adult type
Q61.3 Polycystic kidney, unspecified
Q61.4 Renal dysplasia
Incl.:
Multicystic:
  • dyplastic kidney
  • kidney (developmental)
  • kidney disease
  • renal dysplasia
Excl.:
polycystic kidney disease ( Q61.1-Q61.3)
Q61.5 Medullary cystic kidney
Incl.:
Sponge kidney NOS
Q61.8 Other cystic kidney diseases
Incl.:
Fibrocystic:
  • kidney
  • renal degeneration or disease
Q61.9 Cystic kidney disease, unspecified
Incl.:
Meckel-Gruber syndrome

Q62 Congenital obstructive defects of renal pelvis and congenital malformations of ureter

Q62.0 Congenital hydronephrosis
Q62.1 Atresia and stenosis of ureter
Incl.:
Congenital occlusion of:
  • ureter
  • ureteropelvic junction
  • ureterovesical orifice
Impervious ureter
Q62.2 Congenital megaloureter
Incl.:
Congenital dilatation of ureter
Q62.3 Other obstructive defects of renal pelvis and ureter
Incl.:
Congenital ureterocele
Q62.4 Agenesis of ureter
Incl.:
Absent ureter
Q62.5 Duplication of ureter
Incl.:
  • Accessory
  • Double
  • ureter
Q62.6 Malposition of ureter
Incl.:
  • Deviation
  • Displacement
  • Ectopic
  • Implantation, anomalous
  • (of) ureter or ureteric orifice
Q62.7 Congenital vesico-uretero-renal reflux
Q62.8 Other congenital malformations of ureter
Incl.:
Anomaly of ureter NOS

Q63 Other congenital malformations of kidney

Excl.:
congenital nephrotic syndrome ( N04.-)
Q63.0 Accessory kidney
Q63.1 Lobulated, fused and horseshoe kidney
Q63.2 Ectopic kidney
Incl.:
Congenital displaced kidney
Malrotation of kidney
Q63.3 Hyperplastic and giant kidney
Q63.8 Other specified congenital malformations of kidney
Incl.:
Congenital renal calculi
Q63.9 Congenital malformation of kidney, unspecified

Q64 Other congenital malformations of urinary system

Q64.0 Epispadias
Excl.:
hypospadias ( Q54.-)
Q64.1 Exstrophy of urinary bladder
Incl.:
Ectopia vesicae
Extroversion of bladder
Q64.2 Congenital posterior urethral valves
Q64.3 Other atresia and stenosis of urethra and bladder neck
Incl.:
Congenital:
  • bladder neck obstruction
  • stricture of:
    • —  urethra
    • —  urinary meatus
    • —  vesicourethral orifice
Impervious urethra
Q64.4 Malformation of urachus
Incl.:
Cyst of urachus
Patent urachus
Prolapse of urachus
Q64.5 Congenital absence of bladder and urethra
Q64.6 Congenital diverticulum of bladder
Q64.7 Other congenital malformations of bladder and urethra
Incl.:
Accessory:
  • bladder
  • urethra
Congenital:
  • hernia of bladder
  • malformation of bladder or urethra NOS
  • prolapse of:
    • —  bladder (mucosa)
    • —  urethra
    • —  urinary meatus
  • urethrorectal fistula
Double:
  • urethra
  • urinary meatus
Q64.8 Other specified congenital malformations of urinary system
Q64.9 Congenital malformation of urinary system, unspecified
Incl.:
  • Congenital:
    • anomaly
    • deformity
  • NOS of urinary system