Q00 Anencephaly and similar malformations

Q00.0 Anencephaly

Incl.:

Acephaly

Acrania

Amyelencephaly

Hemianencephaly

Hemicephaly

Q00.1 Craniorachischisis

Q00.2 Iniencephaly

Q01 Encephalocele

Incl.:

encephalomyelocele

hydroencephalocele

hydromeningocele, cranial

meningocele, cerebral

meningoencephalocele

Excl.:

Meckel-Gruber syndrome ( Q61.9)

Q01.0 Frontal encephalocele

Q01.1 Nasofrontal encephalocele

Q01.2 Occipital encephalocele

Q01.8 Encephalocele of other sites

Q01.9 Encephalocele, unspecified

Q02 Microcephaly

Incl.:

Hydromicrocephaly

Micrencephalon

Excl.:

Meckel-Gruber syndrome ( Q61.9)

Q03 Congenital hydrocephalus

Incl.:

hydrocephalus in newborn

Excl.:

Arnold-Chiari syndrome ( Q07.0)

hydrocephalus:

• acquired NOS (G91.-)
• acquired, of newborn (P91.7)
• due to congenital toxoplasmosis (P37.1)
• with spina bifida (Q05.0-Q05.4)

Q03.0 Malformations of aqueduct of Sylvius

Incl.:

Aqueduct of Sylvius:

• anomaly
• obstruction, congenital
• stenosis

Q03.1 Atresia of foramina of Magendie and Luschka

Incl.:

Dandy-Walker syndrome

Q03.8 Other congenital hydrocephalus

Q03.9 Congenital hydrocephalus, unspecified

Q04 Other congenital malformations of brain

Excl.:

cyclopia ( Q87.0)

macrocephaly ( Q75.3)

Q04.0 Congenital malformations of corpus callosum

Incl.:

Agenesis of corpus callosum

Q04.1 Arhinencephaly

Q04.2 Holoprosencephaly

Q04.3 Other reduction deformities of brain

Incl.:

Absence Agenesis Aplasia Hypoplasia

of part of brain

Agyria

Hydranencephaly

Lissencephaly

Microgyria

Pachygyria

Excl.:

congenital malformations of corpus callosum ( Q04.0)

Q04.4 Septo-optic dysplasia

Q04.5 Megalencephaly

Q04.6 Congenital cerebral cysts

Incl.:

Porencephaly

Schizencephaly

Excl.:

acquired porencephalic cyst ( G93.0)

Q04.8 Other specified congenital malformations of brain

Incl.:

Macrogyria

Q04.9 Congenital malformation of brain, unspecified

Incl.:

Congenital: anomaly deformity disease or lesion multiple anomalies

NOS of brain

Q05 Spina bifida

Incl.:

hydromeningocele (spinal)

meningocele (spinal)

meningomyelocele

myelocele

myelomeningocele

rachischisis

spina bifida (aperta)(cystica)

syringomyelocele

Excl.:

Arnold-Chiari syndrome ( Q07.0)

spina bifida occulta ( Q76.0)

Q05.0 Cervical spina bifida with hydrocephalus

Q05.1 Thoracic spina bifida with hydrocephalus

Incl.:

Spina bifida: dorsal thoracolumbar

with hydrocephalus

Q05.2 Lumbar spina bifida with hydrocephalus

Incl.:

Lumbosacral spina bifida with hydrocephalus

Q05.3 Sacral spina bifida with hydrocephalus

Q05.4 Unspecified spina bifida with hydrocephalus

Q05.5 Cervical spina bifida without hydrocephalus

Q05.6 Thoracic spina bifida without hydrocephalus

Incl.:

Spina bifida:

• dorsal NOS
• thoracolumbar NOS

Q05.7 Lumbar spina bifida without hydrocephalus

Incl.:

Lumbosacral spina bifida NOS

Q05.8 Sacral spina bifida without hydrocephalus

Q05.9 Spina bifida, unspecified

Q06 Other congenital malformations of spinal cord

Q06.0 Amyelia

Q06.1 Hypoplasia and dysplasia of spinal cord

Incl.:

Atelomyelia

Myelatelia

Myelodysplasia of spinal cord

Q06.2 Diastematomyelia

Q06.3 Other congenital cauda equina malformations

Q06.4 Hydromyelia

Incl.:

Hydrorachis

Q06.8 Other specified congenital malformations of spinal cord

Q06.9 Congenital malformation of spinal cord, unspecified

Incl.:

Congenital: anomaly deformity disease or lesion

NOS of spinal cord or meninges

Q07 Other congenital malformations of nervous system

Excl.:

familial dysautonomia [Riley-Day] ( G90.1)

neurofibromatosis (nonmalignant) ( Q85.0)

Q07.0 Arnold-Chiari syndrome

Q07.8 Other specified congenital malformations of nervous system

Incl.:

Agenesis of nerve

Displacement of brachial plexus

Jaw-winking syndrome

Marcus Gunn syndrome

Q07.9 Congenital malformation of nervous system, unspecified

Incl.:

Congenital: anomaly deformity disease or lesion

NOS of nervous system