D70 Agranulocytosis

NCCS

DChS.I.1

Incl.:

Agranulocytic angina

Infantile genetic agranulocytosis

Kostmann disease

Neutropenia:

• NOS
• congenital
• cyclic
• drug-induced
• periodic
• splenic (primary)
• toxic

Neutropenic splenomegaly

Werner-Schultz disease

Coding-Hint

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.:

transient neonatal neutropenia ( P61.5)

D71 Functional disorders of polymorphonuclear neutrophils

Incl.:

Cell membrane receptor complex [CR3] defect

Chronic (childhood) granulomatous disease

Congenital dysphagocytosis

Progressive septic granulomatosis

D72 Other disorders of white blood cells

Excl.:

basophilia ( D75.8)

immunity disorders ( D80-D89)

neutropenia ( D70)

abnormal white blood cells (count) ( R72)

preleukaemia (syndrome) ( D46.9)

D72.0 Genetic anomalies of leukocytes

Incl.:

Anomaly (granulation)(granulocyte) or syndrome:

• Alder
• May-Hegglin
• Pelger-Huët

Hereditary:

• leukocytic:
  • —  hypersegmentation
  • —  hyposegmentation
• leukomelanopathy

Excl.:

Chediak(-Steinbrinck)-Higashi syndrome ( E70.3)

D72.1 Eosinophilia

Incl.:

Eosinophilia:

• allergic
• hereditary

D72.8 Other specified disorders of white blood cells

Incl.:

Leukaemoid reaction:

• lymphocytic
• monocytic
• myelocytic

Leukocytosis

Lymphocytosis (symptomatic)

Lymphopenia

Monocytosis (symptomatic)

Plasmacytosis

D72.9 Disorder of white blood cells, unspecified

D73 Diseases of spleen

D73.0 Hyposplenism

Incl.:

Asplenia, postsurgical

Atrophy of spleen

Excl.:

asplenia (congenital) ( Q89.0)

D73.1 Hypersplenism

Excl.:

splenomegaly:

• NOS (R16.1)
• congenital (Q89.0)

D73.2 Chronic congestive splenomegaly

D73.3 Abscess of spleen

D73.4 Cyst of spleen

D73.5 Infarction of spleen

Incl.:

Splenic rupture, nontraumatic

Torsion of spleen

Excl.:

traumatic rupture of spleen ( S36.0)

D73.8 Other diseases of spleen

Incl.:

Fibrosis of spleen NOS

Perisplenitis

Splenitis NOS

D73.9 Disease of spleen, unspecified

D74 Methaemoglobinaemia

D74.0 Congenital methaemoglobinaemia

Incl.:

Congenital NADH-methaemoglobin reductase deficiency

Haemoglobin-M [Hb-M] disease

Methaemoglobinaemia, hereditary

D74.8 Other methaemoglobinaemias

Incl.:

Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)

Toxic methaemoglobinaemia

Coding-Hint

Use additional external cause code (Chapter XX), if desired, to identify cause.

D74.9 Methaemoglobinaemia, unspecified

D75 Other diseases of blood and blood-forming organs

Excl.:

enlarged lymph nodes ( R59.-)

hypergammaglobulinaemia NOS ( D89.2)

lymphadenitis:

• NOS (I88.9)
• acute (L04.-)
• chronic (I88.1)
• mesenteric (acute)(chronic) (I88.0)

D75.0 Familial erythrocytosis

Incl.:

Polycythaemia:

• benign
• familial

Excl.:

hereditary ovalocytosis ( D58.1)

D75.1 Secondary polycythaemia

Incl.:

Erythrocytosis NOS

Polycythaemia:

• NOS
• acquired
• due to:
  • —  erythropoietin
  • —  fall in plasma volume
  • —  high altitude
  • —  stress
• emotional
• hypoxaemic
• nephrogenous
• relative

Excl.:

polycythaemia:

• neonatorum (P61.1)
• vera (D45)

D75.8 Other specified diseases of blood and blood-forming organs

Incl.:

Basophilia

D75.9 Disease of blood and blood-forming organs, unspecified

D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

Excl.:

(Abt-)Letterer-Siwe disease ( C96.0)

eosinophilic granuloma ( C96.6)

Hand-Schüller-Christian disease ( C96.5)

histiocytic sarcoma ( C96.8)

histiocytosis X, multifocal ( C96.5)

histiocytosis X, unifocal ( C96.6)

Langerhans-cell histiocytosis, multifocal ( C96.5)

Langerhans-cell histiocytosis, unifocal ( C96.6)

malignant histiocytosis ( C96.8)

reticuloendotheliosis:

• leukaemic (C91.4)
• nonlipid (C96.0)

reticulosis:

• histiocytic medullary (C96.8)
• lipomelanotic (I89.8)
• malignant NOS (C86.0)

D76.1 Haemophagocytic lymphohistiocytosis

Incl.:

Familial haemophagocytic reticulosis

Histiocytoses of mononuclear phagocytes

D76.2 Haemophagocytic syndrome, infection-associated

Coding-Hint

Use additional code, if desired, to identify infectious agent or disease.

D76.3 Other histiocytosis syndromes

Incl.:

Reticulohistiocytoma (giant-cell)

Sinus histiocytosis with massive lymphadenopathy

Xanthogranuloma

D77* Other disorders of blood and blood-forming organs in diseases classified elsewhere

Incl.:

Fibrosis of spleen in schistosomiasis [bilharziasis] ( B65.-†)