Chapter III
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
(D50-D89)

Other diseases of blood and blood-forming organs
(D70-D77)

D70 Agranulocytosis

Incl.:
Agranulocytic angina
Infantile genetic agranulocytosis
Kostmann disease
Neutropenia:
  • NOS
  • congenital
  • cyclic
  • drug-induced
  • periodic
  • splenic (primary)
  • toxic
Neutropenic splenomegaly
Werner-Schultz disease
Coding-Hint
Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.
Excl.:
transient neonatal neutropenia ( P61.5)

D71 Functional disorders of polymorphonuclear neutrophils

Incl.:
Cell membrane receptor complex [CR3] defect
Chronic (childhood) granulomatous disease
Congenital dysphagocytosis
Progressive septic granulomatosis

D72 Other disorders of white blood cells

Excl.:
basophilia ( D75.8)
immunity disorders ( D80-D89)
neutropenia ( D70)
abnormal white blood cells (count) ( R72)
preleukaemia (syndrome) ( D46.9)
D72.0 Genetic anomalies of leukocytes
Incl.:
Anomaly (granulation)(granulocyte) or syndrome:
  • Alder
  • May-Hegglin
  • Pelger-Huët
Hereditary:
  • leukocytic:
    • —  hypersegmentation
    • —  hyposegmentation
  • leukomelanopathy
Excl.:
Chediak(-Steinbrinck)-Higashi syndrome ( E70.3)
D72.1 Eosinophilia
Incl.:
Eosinophilia:
  • allergic
  • hereditary
D72.8 Other specified disorders of white blood cells
Incl.:
Leukaemoid reaction:
  • lymphocytic
  • monocytic
  • myelocytic
Leukocytosis
Lymphocytosis (symptomatic)
Lymphopenia
Monocytosis (symptomatic)
Plasmacytosis
D72.9 Disorder of white blood cells, unspecified

D73 Diseases of spleen

D73.0 Hyposplenism
Incl.:
Asplenia, postsurgical
Atrophy of spleen
Excl.:
asplenia (congenital) ( Q89.0)
D73.1 Hypersplenism
Excl.:
splenomegaly:
D73.2 Chronic congestive splenomegaly
D73.3 Abscess of spleen
D73.4 Cyst of spleen
D73.5 Infarction of spleen
Incl.:
Splenic rupture, nontraumatic
Torsion of spleen
Excl.:
traumatic rupture of spleen ( S36.0)
D73.8 Other diseases of spleen
Incl.:
Fibrosis of spleen NOS
Perisplenitis
Splenitis NOS
D73.9 Disease of spleen, unspecified

D74 Methaemoglobinaemia

D74.0 Congenital methaemoglobinaemia
Incl.:
Congenital NADH-methaemoglobin reductase deficiency
Haemoglobin-M [Hb-M] disease
Methaemoglobinaemia, hereditary
D74.8 Other methaemoglobinaemias
Incl.:
Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)
Toxic methaemoglobinaemia
Coding-Hint
Use additional external cause code (Chapter XX), if desired, to identify cause.
D74.9 Methaemoglobinaemia, unspecified

D75 Other diseases of blood and blood-forming organs

Excl.:
enlarged lymph nodes ( R59.-)
hypergammaglobulinaemia NOS ( D89.2)
lymphadenitis:
D75.0 Familial erythrocytosis
Incl.:
Polycythaemia:
  • benign
  • familial
Excl.:
hereditary ovalocytosis ( D58.1)
D75.1 Secondary polycythaemia
Incl.:
Erythrocytosis NOS
Polycythaemia:
  • NOS
  • acquired
  • due to:
    • —  erythropoietin
    • —  fall in plasma volume
    • —  high altitude
    • —  stress
  • emotional
  • hypoxaemic
  • nephrogenous
  • relative
Excl.:
polycythaemia:
D75.8 Other specified diseases of blood and blood-forming organs
Incl.:
Basophilia
D75.9 Disease of blood and blood-forming organs, unspecified

D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

Excl.:
(Abt-)Letterer-Siwe disease ( C96.0)
eosinophilic granuloma ( C96.6)
Hand-Schüller-Christian disease ( C96.5)
histiocytic sarcoma ( C96.8)
histiocytosis X, multifocal ( C96.5)
histiocytosis X, unifocal ( C96.6)
Langerhans-cell histiocytosis, multifocal ( C96.5)
Langerhans-cell histiocytosis, unifocal ( C96.6)
malignant histiocytosis ( C96.8)
reticuloendotheliosis:
reticulosis:
  • histiocytic medullary (C96.8)
  • lipomelanotic (I89.8)
  • malignant NOS (C86.0)
D76.1 Haemophagocytic lymphohistiocytosis
Incl.:
Familial haemophagocytic reticulosis
Histiocytoses of mononuclear phagocytes
D76.2 Haemophagocytic syndrome, infection-associated
Coding-Hint
Use additional code, if desired, to identify infectious agent or disease.
D76.3 Other histiocytosis syndromes
Incl.:
Reticulohistiocytoma (giant-cell)
Sinus histiocytosis with massive lymphadenopathy
Xanthogranuloma

D77* Other disorders of blood and blood-forming organs in diseases classified elsewhere

Incl.:
Fibrosis of spleen in schistosomiasis [bilharziasis] ( B65.-†)